Cell short-chain fatty acyl-CoA dehydrogenase (ACYL COA DEHYDROGENASE) activity colorimetric method quantitative detection kit 英文别名: 中文名: 细胞短链脂酰辅酶A脱氢酶(ACYL COA DEHYDROGENASE)活性比色法定量检测试剂盒 中文别名: 细胞短链脂酰辅酶A脱氢酶(ACYL COA DEHYDROGENASE)活性比色法定量检测试剂盒 ...
Verity MA, Turnbull DM 1993 Assay of acyl-CoA dehydrogenase activity in frozen muscle biopsies: application to medium-chain acyl-CoA dehydrogenase deficiency. Biochem Med Metab Biol 49:351-362Verity, MA, Turnbull, DM (1993) Assay of acyl-CoA dehydrogenase activity in frozen muscle biopsies: ...
A SIMPLE ASSAY FOR MEDIUM CHAIN ACYL-COA DEHYDROGENASE (MCADH) ACTIVITY IN DICARBOXYLIC ACIDURIA (DCA) FIBROBLASTSDCA, an inborn error of 尾-oxidation, is due to MCADH deficiency, since we found MCADH activity in DCA fibroblast mitochondrial sonic supernatants (MS) to be 5% of control with ...
Quijada-Fraile P, Bellusci M, Moráis A, Pedrón-Giner C, Rausell D, Correcher P, Unceta M, Stanescu S, Ugarte M, Ruiz-Sala P, Pérez B. Lymphocyte Medium-Chain Acyl-CoA Dehydrogenase Activity and Its Potential as a Diagnostic Confirmation Tool in Newborn Screening Cases. Journal of cl...
Crystal structures of medium-chain acyl-CoA dehydrogenase from pig liver mitochondria with and without substrate. The three-dimensional structure of medium-chain acyl-CoA dehydrogenase from pig mitochondria in the native form and that of a complex of the enzyme and a s... J,J,Kim,... - 《...
Acyl-CoA dehydrogenases constitute a family of flavoproteins that catalyze the α,β-dehydrogenation of fatty acid acyl-CoA conjugates. While they differ widely in their specificity, they share the same basic chemical mechanism of α,β-dehydrogenation. Medium chain acyl-CoA dehydrogenase is probably...
Most of the ATP generated in cells arises from the β-oxidation of fatty acids. As shown inScheme 1, the first step of the β-oxidation of fatty acids located in the mitochondrial matrix is catalysed by the FAD cofactor of acyl-CoA dehydrogenase, which oxidizes fatty acyl CoA thereby reduci...
ydrogenase activity Recurrent Reye-like syndrome with normal long and medium chain acyl-CoA-dehydrogenase activityRecurrent Reye-like syndrome with normal long and medium chain acyl-CoA-dehydrogenase activityM.H., MarandianA., SoltanabadiM., Rakchan...
Depending on the desired product form, different β-oxidation steps are targeted (e.g., acyl-CoA dehydrogenase, FadE, for fatty alcohol production; thiolase, FadA/FadI, for methyl ketone production) to produce the substrate for termination enzymes (e.g., saturated acyl-CoA for acyl-CoA ...
Among the four enzymes, hLCAD exhibited the lowest palmitoyl-CoA dehydrogenase activity (Fig. 2A) but the highest rate of H2O2 formation (Fig. 2B). mLCAD, which is 88% identical in amino acid sequence, produced only half as much H2O2 as hLCAD but was twice as active as a dehydrogenase....