组织长链脂酰辅酶A脱氢酶(ACYL COA DEHYDROGENASE)活性比色法定量检测试剂盒 CAS号: 英文名: Colorimetric quantitative detection kit for tissue long-chain acyl-CoA dehydrogenase (ACYL COA DEHYDROGENASE) activity英文别名: Colorimetric quantitative detection kit for tissue long-chain acyl-CoA dehydrogenase (...
Taylor RW, Jackson S, Pourfarzam M, Bartlett K, Turnbull DM (1992) Measurement of acyl-CoA dehydrogenase activity in cultured skin fibroblasts and blood platelets. J Inher Metab Dis 15 : 727-732.Measurement of acyl-CoA dehydrogenase activity in cultured skin fibroblasts and blood platelets - ...
Assay of Acyl-CoA Dehydrogenase Activity in Frozen Muscle Biopsies: Application to Medium-Chain Acyl-CoA Dehydrogenase Deficiency 来自 Elsevier 喜欢 0 阅读量: 28 作者:A M.,Verity,and,M D.,Turnbull 摘要: The acyl-CoA dehydrogenases (ACDs) are mitochondrial enzymes that dehydrogenate acyl-...
英文名称: Cell short-chain fatty acyl-CoA dehydrogenase (ACYL COA DEHYDROGENASE) activity colorimetric method quantitative detection kit 英文同义词: CAS号: 分子式: 分子量: 0 EINECS号: Mol文件: Mol File 细胞短链脂酰辅酶A脱氢酶(ACYL COA DEHYDROGENASE)活性比色法定量检测试剂盒 信息错误报告 提...
A SIMPLE ASSAY FOR MEDIUM CHAIN ACYL-COA DEHYDROGENASE (MCADH) ACTIVITY IN DICARBOXYLIC ACIDURIA (DCA) FIBROBLASTSDCA, an inborn error of 尾-oxidation, is due to MCADH deficiency, since we found MCADH activity in DCA fibroblast mitochondrial sonic supernatants (MS) to be 5% of control with ...
Acyl-CoA dehydrogenase activity in the riboflavin-deficient rat. Effects of starvation Riboflavin deficiency in weanling rats causes a metabolic disorder characterized by failure to oxidize fatty acids. The disorder is similar to that seen in... NS Ross,CL Hoppel - 《Biochemical Journal》 被引量:...
ydrogenase activity Recurrent Reye-like syndrome with normal long and medium chain acyl-CoA-dehydrogenase activityRecurrent Reye-like syndrome with normal long and medium chain acyl-CoA-dehydrogenase activityM.H., MarandianA., SoltanabadiM., Rakchan...
Most of the ATP generated in cells arises from the β-oxidation of fatty acids. As shown inScheme 1, the first step of the β-oxidation of fatty acids located in themitochondrial matrixis catalysed by the FADcofactorof acyl-CoAdehydrogenase, which oxidizes fatty acyl CoA thereby reducing FAD...
Medium-Chain Acyl-CoA Dehydrogenase Deficiency Confirmatory Testing Confirmatory testing involves urinary organic acid levels, repeating the acylcarnitine profile on plasma, MCAD enzyme activity levels, and genotype analysis via chromosomal testing.
In the studies with the bacterial SCAD, the ratio of oxidase to dehydrogenase activity increases as the size of the CoA analog of the substrate decreases, which is consistent with the idea that the more solvent accessible the reduced flavin is, the higher the oxidase activity becomes [37]. ...