酰基辅酶A氧化酶I缺乏症的英文名字是Acyl-CoA Oxidase I Deficiency。基因解码表明:佳学基因通过基因解码发现:酰基辅酶A氧化酶I缺乏症是由基因突变引起的。这种疾病是由于ACOX1基因的突变导致酰基辅酶A氧化酶I的功能缺陷,从而影响脂肪酸的代谢。ACOX1基因位于人类染色体17号上,突变会导致酰基辅酶A氧化酶I的活性降低或...
Novel subtype of peroxisomal acyl-CoA oxidase deficiency and bifunctional enzyme deficiency with detectable enzyme protein: identification by means of comp... We describe four infants with a novel subtype of an isolated deficiency of one of the peroxisomal beta-oxidation enzymes with detectable enzyme ...
2002. Profiling of acyl-CoA oxidase-deficient and peroxisome proliferator Wy14,643- treated mouse liver protein by surface-enhanced laser desorption/ionization ProteinChip Biology System. Gene Expr 10:165-177.Chu, R., Zhang, W., Lim, H., Yeldandi, A. V., Herring, C., Brumfield, L., ...
Distinction between peroxisomal bifunctional enzyme and acyl-CoA oxidase deficiencies. Ann Neurol 1995; 38(3): 472-7Watkins P, McGuiness M, Raymond G, et al. Distinction between peroxisomal bifunctional enzyme acyl-CoA oxidase deficiencies. Ann Neurol. 1995; 38:473-477....
Acyl-CoA Oxidase 1Argan OilLPSPGC-1αPeroxisome ProliferationP-NALDPPARαPseudo-neonatal adrenoleukodystrophy (P-NALD) is a neurodegenerative disorder caused by acyl-CoA oxidase 1 (ACOX1) deficiency with subsequent impairment of peroxisomal fatty acid β-oxidation, accumulation of very long chain ...
Related to acyl CoA dehydrogenase deficiency:Carnitine deficiency ac·yl (ăs′əl) n.Chemistry An organic group having the general formula RCO-, derived from an organic acid. [ac(id)+-yl.] American Heritage® Dictionary of the English Language, Fifth Edition. Copyright © 2016 by Hough...
英文名称:Acyl-CoA Oxidase/ Acyl-CoA:oxygen-2-oxidoreductase 保质期:长期个月 保存条件:-20℃ 品牌:百奥莱博 规格:500U 产地:国产|进口 编号:QN0378 CAS号:61116-22-1 储存条件:-20℃ 性状:黄色冻干粉 来源:微生物 比活:≥ 30U/mg protein ...
Acyl-CoA Oxidase 酯酰辅酶A氧化酶;CAS号61116-22-1;试剂级 价格电议 起批量≥1 毫克 最小起订1毫克 供货总量500000毫克 发货地址北京市海淀区 建议售价￥电议 更新日期2024年12月06日 产品规格500U 即时洽谈立即询价查看联系方式 收藏产品发送留言
细胞长链脂酰辅酶A氧化酶(acyl-CoAoxidase)活性比色法定量检测试剂盒 产品规格: 20次 有效成分含量: 99 检测方法: 比色法 样本: 组织,细胞,线粒体,细菌等 保质期: 6个月 标记物: 血液 储存条件: 冷藏或-20℃ 用途范围: 仅用于科学实验研究使用 是否进口: 否 包装规格: 盒装 产地: 上海 ...
产品名称 组织长链脂酰辅酶A氧化酶(acyl-CoAoxidase)活性比色法定量检测试剂盒 产品规格 20次 有效成分含量 99 检测方法 荧光定量 样本 组织,细胞,线粒体,细菌等 保质期 6个月 标记物 血液 储存条件 冷藏或-20℃ 用途范围 仅用于科学实验研究使用 是否进口 否 包装规格 盒装 售价 客服报价为准 ...