英文名称:3-Hydroxydecanoyl(R)-CarnitineInnerSalt(MixtureofDiastereomers) CAS:1245943-08-1 纯度:NULL 包装信息:10mg;1mg;2.5mg;5mg 备注:NULL 佛山合硕医药科技有限公司 联系电话: 15363639686 产品介绍: 中文名称:3-羟基癸酰基-L-肉碱 3- 英文名称:Hydroxydecanoyl-L-Carnitine ...
2.血酰基肉碱谱分析患者可表现为豆蔻羟酰基肉碱(3-hydromyristoylcarnitine,C14-OH)、棕榈羟酰基肉碱(3-Hydroxy-hexadecanoylcarnitine,C16-OH)、棕榈羟烯酰基肉碱(3-Hydroxy-hexadecenoylcarnitine,C16:1-OH)、油酸羟酰基肉碱(3-Hydroxy-octadecanoylcarnitine,C18:OH)和油酸羟烯酰基肉碱(3-Hydroxy-octadecenoylcarnitine...
肌型患者可有肌红蛋白尿。 2.血酰基肉碱谱分析患者可表现为豆蔻羟酰基肉碱(3-hydromyristoylcarnitine,C14-OH)、棕榈羟酰基肉碱(3-Hydroxy-hexadecanoylcarnitine,C16-OH)、棕榈羟烯酰基肉碱(3-Hydroxy-hexadecenoylcarnitine,C16:1-OH)、油酸羟...
长链-3-羟酰基辅酶A脱氢酶缺乏症(long chain 3-hydroxyacyl-CoA dehydrogenase deficiency,LCHADD)是一种脂肪氧化缺陷的线粒体疾病。是由于编码长链3-羟基辅酶A脱氢酶的基因突变导致的常染色体隐性遗传病。1989年由Wanders首次报道。该病临床表现多样,主要受累脏器有心脏、肝脏和骨骼肌,常 见的症状有低酮性低糖...
4-Dimethylphenylhydrazine hydrochloride97%250g49307个工作日0.25D806441-25ml112-13-0癸酰氯Decanoyl Chloride98%25ml76现货0.025D806441-100ml112-13-0癸酰氯Decanoyl Chloride98%100ml186现货0.1D806441-500ml112-13-0癸酰氯Decanoyl Chloride98%500ml618现货0.5D806442-25mg120014-06-41-苄基-4-[(5,6-二甲氧...
长链-3-羟酰基辅酶A脱氢酶缺乏症诊疗指南(2019年版)2长链-3-羟酰基辅酶A脱氢酶缺乏症概述长链-3-羟酰基辅酶A脱氢酶缺乏症(longchain3-hydroxyacyl-CoAdehydrogenasedeficiency,LCHADD)是一种脂肪氧化缺陷的线粒体疾病。是由于编码长链3-羟基辅酶A脱氢酶的基因突变导致的常染色体隐性遗传病。1989年由Wanders首次报道。
3-hydroxyisovalerylcarnitine C12H23NO5 3-hydroxy-3-ethylglutaryl-coenzyme A 69925-08-2 C28H46N7O20P3S 6-hydroxy-3,4-dihydro-3-(dipropylamino)-2H-1-benzopyran 116005-04-0 C15H23NO2 2-(HYDROXYMETHYL)QUINAZOLIN-4(3H)-ONE C9H8N2O2 2-hydroxybiphenyl monooxygenase 4-hydroxydecanoyl-teicoplan...
2245711-27-5L-十八碳酰肉碱盐酸盐-D3Octadecanoyl-L-carnitine-d3HCL(n-methyl-d3)284487-60-1DL-3-羟基十四烷酸-2,2,3,4,4-D5DL-3-Hydroxymyristicacid-2,2,3,4,4-d5506-30-9UN二十烷酸-12,12,13,13-D4Arachidicacid-12,12,13,13-d4232600-70-3二十烷酸-2,2-D2Arachidicacid-2,2-d...
MCE 站:Decanoyl-L-carnitine-d3 chloride 相关产品:D8-MMAE | VX-984 | BMS-986202 | D8-MMAF hydrochloride | Exatecan D5 mesylate | Remdesivir-D5 | Eldecalcitol-d6 | Omeprazole D3 | Calcitriol D6 | 3-O-Methyldopa D3 | Mycophenolic acid D3 | Osimertinib D6 | Palbociclib D8 | Phenylac...
13C,2H3]-L-Acetylcarnitine chloride salt13C,2H3]-L-乙酰肉碱氯化物盐5080-50-2 13C]-Benzyl alcohol13C]-苄醇54522-91-7 Man-6MAN-6 D-[3-13C]galactoseD-[3-13C]半乳糖478518-56-8 4-Methylcatechol4-甲基儿茶酚452-86-8 DL-threo-PDMP hydrochlorideD,L-THREO-1-PHENYL-2-DECANOYLAMINO-...